Evaluation and Management of Total Colonic Hirschsprung Disease: A Comprehensive Review From the American Pediatric Surgical Association (APSA) Hirschsprung Disease Interest Group

In brief

This comprehensive review from APSA's Hirschsprung Disease Interest Group addresses the diagnostic and therapeutic challenges unique to total colonic Hirschsprung disease (TCHD). It offers expert consensus on perioperative management strategies for this complex patient population requiring specialized surgical care.

• TCHD patients require specialized pre- and postoperative management distinct from standard Hirschsprung disease protocols.
• Expert consensus provides a rational diagnostic framework for identifying total colonic aganglionosis in pediatric patients.
• APSA guidelines offer evidence-based surgical approaches tailored to the unique challenges of TCHD management.
• Multidisciplinary care coordination is essential for optimizing outcomes in children with total colonic involvement.

Written by the GCMD Library team from the article.