Outcomes of Kasai Portoenterostomy in Patients With Congenital Heart Disease: A Silent Comorbidity

jpedsurg.org

Biliary atresia (BA) is the most common cause of end-stage liver disease in children. Around 5 %–15 % of patients with BA have a congenital heart disease (CHD) diagnosis. Despite high prevalence of a CHD diagnosis in patients with BA, outcomes of Kasai portoenterostomy (KPE) in the CHD population remain unexplored.

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Article · Mar 2025 · 1 min read

In brief

This study examines surgical outcomes of Kasai portoenterostomy in biliary atresia patients who have coexisting congenital heart disease, a comorbidity present in 5-15% of cases but rarely studied. The research addresses a critical knowledge gap in managing this complex pediatric population with dual organ system involvement.

Biliary atresia is the leading cause of end-stage liver disease in pediatric patients.
5-15% of biliary atresia patients have concomitant congenital heart disease, yet outcomes data for this subset remain limited.
Kasai portoenterostomy outcomes in patients with concurrent CHD are poorly characterized and warrant further investigation.

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