The Right Colon Patch Pull-through for Total Colonic Aganglionosis: A Systematic Review

In brief

This systematic review examines the right colon patch pull-through technique for treating total colonic aganglionosis, a rare variant of Hirschsprung disease. The review addresses the limited evidence comparing surgical approaches and evaluates whether this specific technique offers physiological advantages over alternative procedures.

• Total colonic aganglionosis is a rare Hirschsprung variant requiring specialized surgical approaches beyond standard pull-through techniques.
• Right colon patch pull-through preserves ileocecal valve function, potentially improving postoperative bowel control compared to other TCA repairs.
• Current evidence for RCP technique is limited by small case series and lack of comparative studies across surgical approaches.
• Surgical decision-making in TCA must balance anatomical preservation with adequate resection of aganglionic bowel segments.
• Long-term functional outcomes (continence, stooling patterns) remain the critical metric for comparing TCA surgical techniques.

Written by the GCMD Library team from the article.