Unicentric Series of 82 Consecutive Patients With Ultralong Hirschsprung Disease: How Experience Leads Management

In brief

This study presents the largest single-center series of 82 patients with ultralong Hirschsprung disease variants (total colonic, extended, and total intestinal aganglionosis). The authors share their institutional management algorithm developed through extensive experience treating these rare and complex forms of congenital intestinal aganglionosis.

• Ultralong Hirschsprung disease encompasses total colonic, extended, and total intestinal aganglionosis—rare variants requiring specialized management.
• This represents the largest single-center series of 82 consecutive ultralong HSCR patients, providing robust evidence for treatment protocols.
• Institutional experience is critical for optimizing surgical outcomes in these complex aganglionosis cases.
• A standardized management algorithm can guide decision-making for ultralong HSCR at specialized digestive disease centers.
• Consecutive patient series allow for systematic evaluation of surgical techniques and long-term outcomes in rare HSCR variants.

Written by the GCMD Library team from the article.