CAPS - Educational Outcomes in School Age Children with a History of Hirschsprung’s Disease - Michael Cowap
Hirschsprung disease is a loss of innervation to a section of bowel
Hirschsprung disease is sometimes associated with genetic syndromes such as Down syndrome
Hirschsprung disease can be fixed but requires surgery that involves cutting that section of bowel out
Children with Hirschsprung disease may have ongoing issues with constipation, incontinence, and occasional abdominal pain after surgery
The study compared children with Hirschsprung disease to their peers in real-world assessments
While there may be some delay in the beginning in the preschool assessment, once children with Hirschsprung start school, there does not appear to be a significant difference between them and their peers in assessments that include reading and number skills
There is not a significant difference in graduation from grade 12 between children with Hirschsprung disease and their peers
Neurodevelopmental outcomes are just as important to parents as what surgeons do directly in the operating room
Expert opinionPam Choi3:34
Data was only specifically from Manitoba and using a Manitoba health repository
The standardized tests are standardized within each province
The data includes public school, private school and homeschooling
First Nations and indigenous schools were not included in the repository
The study did not account for how the disease is affecting each child individually
Patients were matched based on being male and socioeconomic status
The data was from 1997 to 2012
The study did not include a subset analysis of long segment Hirschsprung disease
Panel Discussion and Case Presentation Part I: Pediatric Bowel Management 2013
The sacral ratio correlates with prognosis for bowel control in anorectal malformation patients
Normal sacral ratio is 0.7 or more, indicating good prognosis for bowel control
Sacral ratio of 0.4 or less means the patient will be fecally incontinent regardless of malformation type
No patient with sacral ratio less than 0.4 has ever been observed to be fecally continent
Patients with sacral ratio 0.4 or less will need enemas for life
The only indication for permanent colostomy is incapacity to form solid stool
Bad prognosis for bowel control does not mean the patient is a candidate for permanent colostomy
Patients subjected to bowel management report better quality of life than having a colostomy
With incapacity to form solid stool there is no bowel management option
Patients with Down syndrome and anorectal malformation have 80% chance of bowel control
Most patients with Down syndrome have anorectal malformation without fistula
Host summaryThe host summarizing the discussion — not the host's own clinical position8:01
Only 15% of patients with rectal bladder neck fistula have bowel control
Rectal perineal fistula is the malformation with the best prognosis for bowel control
Good prognosis depends upon having a good operation, good sacrum, and no tethered cord