StayCurrentMD · Endoscopic Treatment of Craniosynostosis: Pediatric Endoscopic Neurosurgery 2018
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Video34 min·Published Jan 2018Older

Endoscopic Treatment of Craniosynostosis: Pediatric Endoscopic Neurosurgery 2018

With Dr. Mark Proctor · StayCurrentMD
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What the experts said53 expert statements
Human skull is made up of 5 major bones separated by growth plates called sutures.
ClinicalMark Proctor
Humans have very rapid brain growth in the first year of life, slowing considerably over the second year; past 2 years of age sutures play a very small role in skull or brain growth.
ClinicalMark Proctor
Virchow's law defines that skull growth is normally perpendicular to the sutures; if bone is closed, growth occurs parallel to sutures due to compensatory overgrowth in other areas.
ClinicalMark Proctor
Synostosis affects about 1 in every 2000 live births, with sagittal being by far the most common in about half of children.
EpidemiologicalMark Proctor
In sagittal synostosis, the back of the head is the narrowest part (whereas normally it is the widest), with wide and bossed frontal region.
ClinicalMark Proctor
In unilateral coronal synostosis, there is orbital dystopia where the orbit on the affected side is higher and shallower, and the nose deviates toward the affected side.
ClinicalMark Proctor
Lambdoid synostosis is very rare, representing about 1 to 2% of all synostosis cases; Boston Children's sees about 100 new synostosis patients per year and averages 1 lambdoid case annually.
EpidemiologicalMark Proctor
In lambdoid synostosis, the mastoid should be low (extended) on the affected side, which helps distinguish it from deformational changes.
ClinicalMark Proctor
Strip craniectomy results were poor historically, with about one-third of patients having bones fuse together before significant correction, leading to adoption of larger cranial vault reconstructions.
ClinicalMark Proctor
David Jimenez and Constance Barone in the mid-1990s pioneered endoscopic synostosis surgery with smaller incisions, less blood loss, and adjuvant helmet therapy.
ClinicalMark Proctor
Open surgery is a mechanical operation where bones are repositioned and fixed, but those bones don't grow normally over time; results at end of surgery aren't completely predictive of outcomes 5 or 10 years later.
ClinicalMark Proctor
Endoscopic surgery is a release procedure that relies on brain growth to move bones out over time or requires adjuncts like springs, distractors, or helmets to direct growth.
ClinicalMark Proctor
Conceptually, endoscopic surgery turns synostosis into a deformational problem by opening bones to make them malleable, then reshaping with a helmet.
ClinicalMark Proctor
Laparoscopic cholecystectomy was first reported in 1987 by a team in France and met significant early skepticism before becoming standard of care.
ClinicalMark Proctor
Only surgeons involved with open cholecystectomy and management of its potential complications should perform laparoscopic cholecystectomy (quote from historical article applied to craniosynostosis context).
OpinionMark Proctor
CDC parameters of care for synostosis (2010–2012) consider endoscopic surgery a viable treatment option but stress the need for a very experienced team.
GuidelineMark Proctor
For sagittal synostosis endoscopic surgery, a 0-degree endoscope is used; Proctor avoids using high-quality neurosurgical scopes to prevent damage in this relatively blunt procedure.
ClinicalMark Proctor
Meticulous technique is necessary to keep blood transfusion rates down in endoscopic craniosynostosis surgery.
ClinicalMark Proctor
For sagittal synostosis, two incisions are made (anterior and posterior), burr holes created and expanded with Kerrison rongeurs to about a 2 cm gap.
ClinicalMark Proctor
Recent studies from Hopkins, DC, and Saint Louis show that narrow (2 cm) bone strips are just as effective as wide (6 cm) strips; most centers now use narrow strips with no barrel staves.
ClinicalMark Proctor
Helmets allow real-time adjustment (e.g., if top of head is getting flat, can adjust for more rounding), whereas springs or distractors cannot be adjusted.
ClinicalMark Proctor
Endoscopic treatment leads to sustained changes in cranial index over time, with results very similar to open operation from a cranial index perspective (compared by multiple groups).
ClinicalMark Proctor
In unilateral coronal synostosis treated endoscopically, neo-suture formation can occur, making it appear as if the patient never had a fused suture.
ClinicalMark Proctor
3D photogrammetry studies show facial asymmetry improved significantly more in the endoscopic group than in the frontal orbital advancement group, likely due to early release.
ClinicalMark Proctor
Astigmatism improved much better with endoscopic surgery compared to open surgery.
ClinicalMark Proctor
First 100 consecutive endoscopic cases (all synostosis types): mean surgical time 48 minutes, estimated blood loss 23 mL, 8 transfusions, median hospital stay 1 day.
ClinicalMark Proctor
Weight under 5 kg was a risk factor for transfusion; now waiting until over 5 kg for all patients, transfusion rates down to about 3%.
ClinicalMark Proctor
Cost of endoscopic treatment is 40% of open operation; three studies (Boston, Saint Louis, Midwest US) show consistent results.
ClinicalMark Proctor
Boston cost study included all hospital costs, home costs, and gas mileage for families traveling to orthotist appointments.
ClinicalMark Proctor
In experienced centers, both open and endoscopic craniosynostosis surgery should be very safe procedures.
OpinionMark Proctor
Centers should have access to both minimally invasive and open techniques, and provide comprehensive care including surgery, neuropsych testing, and orthotist access.
OpinionMark Proctor
Endoscope exposure to dura during dissection is very brief (20–30 seconds on average for sagittal synostosis); light source typically used at 70–75% (not 100%).
ClinicalMark Proctor
Endoscope appears to generate less heat than the drill; no injuries from scope heat have been observed.
ClinicalMark Proctor
Ideal surgical age for endoscopic craniosynostosis is about 10 to 12 weeks (3 months), when brain growth is most rapid.
ClinicalMark Proctor
Oldest patient treated endoscopically was 7 months of age (mild sagittal synostosis); result was reasonable but correction is less robust at older ages due to reduced brain growth.
ClinicalMark Proctor
Would not offer endoscopic surgery past 6 months for severe deformity (e.g., cranial index 0.62); may extend to 5–6 months for milder cases (cranial index 0.7 or 0.72).
OpinionMark Proctor
Historical strip craniectomy had 20–30% rate of suture closing back before significant correction; current approach differs by using adjuvant therapy (helmets, springs, distractors) to direct growth.
ClinicalMark Proctor
In helmeted sagittal synostosis, the goal is 2:1 growth ratio (width to length) during helmet course; starting cranial index 0.75 reaches about 0.8 after 6 months.
ClinicalMark Proctor
Head circumference must be tracked closely during helmet therapy; do not want to see fall-off on growth curve; ideally should see a jump up with the operation.
ClinicalMark Proctor
Early endoscopic cases used two large IVs and an arterial line (treated like open cases); current standard is two IVs only, no A-line, no Foley catheter.
ClinicalMark Proctor
Some endoscopic craniosynostosis patients could truly go home the same day, though Proctor has never been bold enough to do so; most stay overnight (often as 23-hour observation rather than formal admission).
ClinicalMark Proctor
Average sagittal synostosis case is so classic that most surgeons can diagnose without imaging; imaging obtained if any question exists to avoid operating on open suture or missing a fused suture.
ClinicalMark Proctor
Well under 10–20% of craniosynostosis patients require imaging to make the diagnosis.
ClinicalMark Proctor
For sagittal synostosis, plain X-ray may suffice instead of CT scan; unilateral coronal can almost always be diagnosed on exam (nasal deviation, eye height, ear position).
ClinicalMark Proctor
Would never consider operating on lambdoid synostosis without a CT scan; it is a very difficult diagnosis to make clinically.
OpinionMark Proctor
Ultrasound is increasingly used to show open versus closed sutures without radiation exposure; literature on this is growing.
ClinicalMark Proctor
MRI black-bone studies are a potential viable technique to show suture status and brain detail better than other modalities, though not yet adopted at Boston Children's.
ClinicalMark Proctor
For metopic synostosis, helmet can be stopped as soon as desired shape is achieved (as short as 3 months); there is essentially no regression.
ClinicalMark Proctor
For sagittal synostosis, there is definite regression; patients lose on average 0.02 cranial index between 1 and 2 years of age.
ClinicalMark Proctor
Average helmet duration for sagittal synostosis is 7 months from surgery; Proctor pushes closer to 1 year unless cranial index exceeds 0.82.
ClinicalMark Proctor
For unilateral coronal, there is no regression, but almost none are perfect at 1 year, so helmet is almost always continued to 1 year.
ClinicalMark Proctor
Jimenez now standardly helmets sagittal synostosis patients for 18 months; Proctor thinks loss between 1 and 2 years is so small that helmet value after 1 year is very small.
OpinionMark Proctor
For coronal synostosis, bone removal is also about 1 to 2 centimeters, similar to sagittal.
ClinicalMark Proctor